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Ramsay Hunt syndrome (RHS) type 1 is a rare, degenerative, neurological disorder characterized by myoclonus epilepsy, intention tremor, progressive ataxia and occasionally cognitive impairment 〔(【引用サイトリンク】 Ramsay Hunt Syndrome )〕〔(【引用サイトリンク】 National Institute of Neurological Disorders and Stroke )〕 It has also been alternatively called ''dyssynergia cerebellaris myoclonica'', ''dyssynergia cerebellaris progressiva'', dentatorubral degeneration, or Ramsay Hunt cerebellar syndrome. ==Presentation== Onset of symptoms usually occur in early adulthood and is characterized by intention tremor, progressive ataxia, convulsions, and myoclonic epileptic jerks.〔〔 Tremors usually affect one extremity, primarily the upper limb, and eventually involve the entire voluntary motor system.〔 Overall, the lower extremity is usually disturbed less often than the upper extremity.〔 Additional features of the syndrome include: an unsteady gait, seizures, muscular hypotonia, reduced muscular coordination, asthenia, adiadochokinesia and errors with estimating range, direction, and force of voluntary movements.〔〔 Mental deterioration can occur, however it is rare.〔 抄文引用元・出典: フリー百科事典『 ウィキペディア（Wikipedia）』 ■ウィキペディアで「Ramsay Hunt syndrome type I」の詳細全文を読む スポンサード リンク
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